E. Nusco: search on Z-Library

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1

Intracranial gene delivery of LV-NAGLU vector corrects neuropathology in murine MPS IIIB

Carmela Di Domenico, Guglielmo R.D. Villani, Daniele Di Napoli, Edoardo Nusco, Gaetano Calì, Lucio Nitsch, Paola Di Natale

Journal:

American Journal of Medical Genetics Part A

Year:

2009

Language:

english

File:

PDF, 279 KB

english, 2009

2

The cell cycle: a new entry in the field of Ca2+signaling

L. Santella, E. Ercolano, G. A. Nusco

Journal:

Cellular and Molecular Life Sciences

Year:

2005

Language:

english

File:

PDF, 196 KB

english, 2005

3

Ca2+signalling and membrane current activated by cADPr in starfish oocytes

F. Moccia, G. A. Nusco, D. Lim, E. Ercolano, G. Gragnaniello, E. R. Brown, L. Santella

Journal:

Pflügers Archiv European Journal of Physiology

Year:

2003

Language:

english

File:

PDF, 715 KB

english, 2003

4

Ca2+ Response to cADPr during Maturation and Fertilization of Starfish Oocytes

Gilda A. Nusco, Dmitri Lim, Pawel Sabala, Luigia Santella

Journal:

Biochemical and Biophysical Research Communications

Year:

2002

Language:

english

File:

PDF, 929 KB

english, 2002

5

Modulation of calcium signalling by the actin-binding protein cofilin

Gilda A. Nusco, Jong Tai Chun, Emanuela Ercolano, Dmitry Lim, Gianni Gragnaniello, Keiichiro Kyozuka, Luigia Santella

Journal:

Biochemical and Biophysical Research Communications

Year:

2006

Language:

english

File:

PDF, 1.43 MB

english, 2006

6

T.O. 6 Systemic delta-sarcoglycan gene transfer into cardiomyopathic BIO14.6 hamsters by AAV

C. Vitiello, A. Auricchio, S. Faraso, N. Sorrentino, D. Di Napoli, S. Castaldo, E. Nusco, S. Aurino, V. Saccone, G. Piluso, V. Nigro

Journal:

Neuromuscular Disorders

Year:

2006

Language:

english

File:

PDF, 46 KB

english, 2006

7

G.P.3.02 In vivo biodistribution of non-viral systems for oligoribonucleotides delivery

P. Rimessi, P. Sabatelli, F. Gualandi, P. Spitali, M. Bovolenta, E. Martoni, M. Fabris, V. Nigro, E. Nusco, E. Calzolari, A. Ferlini

Journal:

Neuromuscular Disorders

Year:

2007

Language:

english

File:

PDF, 46 KB

english, 2007

8

NAADP and InsP3 play distinct roles at fertilization in starfish oocytes

Francesco Moccia, Gilda A. Nusco, Dmitry Lim, Keiichiro Kyozuka, Luigia Santella

Journal:

Developmental Biology

Year:

2006

Language:

english

File:

PDF, 868 KB

english, 2006

9

Phenylbutyrate therapy for pyruvate dehydrogenase deficiency

Rosa Ferriero, Eleonora Lamantea, Edoardo Nusco, Luisa Bonafè, Brendan Lee, Massimo Zeviani, Nicola Brunetti-Pierri

Journal:

Year:

2012

Language:

english

File:

PDF, 74 KB

english, 2012

10

Improved Efficacy and Reduced Toxicity by Ultrasound-Guided Intrahepatic Injections of Helper-Dependent Adenoviral Vector in Gunn Rats

Pastore, Nunzia, Nusco, Edoardo, Piccolo, Pasquale, Castaldo, Sigismondo, Vaníkova, Jana, Vetrini, Francesco, Palmer, Donna J., Vitek, Libor, Ng, Philip, Brunetti-Pierri, Nicola

Journal:

Human Gene Therapy Methods

Year:

2013

Language:

english

File:

PDF, 235 KB

english, 2013

11

A highly secreted sulphamidase engineered to cross the blood-brain barrier corrects brain lesions of mice with mucopolysaccharidoses type IIIA

Sorrentino, Nicolina Cristina, D'Orsi, Luca, Sambri, Irene, Nusco, Edoardo, Monaco, Ciro, Spampanato, Carmine, Polishchuk, Elena, Saccone, Paola, De Leonibus, Elvira, Ballabio, Andrea, Fraldi, Alessan

Journal:

EMBO Molecular Medicine

Year:

2013

Language:

english

File:

PDF, 2.03 MB

english, 2013

12

Sustained Reduction of Hyperbilirubinemia in Gunn Rats After Adeno-Associated Virus-Mediated Gene Transfer of Bilirubin UDP-Glucuronosyltransferase Isozyme 1A1 to Skeletal Muscle

Pastore, Nunzia, Nusco, Edoardo, Vaníkova, Jana, Sepe, Rosa Maria, Vetrini, Francesco, McDonagh, Antony, Auricchio, Alberto, Vitek, Libor, Brunetti-Pierri, Nicola

Journal:

Human Gene Therapy

Year:

2012

Language:

english

File:

PDF, 391 KB

english, 2012

13

Tbx1 regulates brain vascularization

Cioffi, S., Martucciello, S., Fulcoli, F. G., Bilio, M., Ferrentino, R., Nusco, E., Illingworth, E.

Journal:

Human Molecular Genetics

Year:

2014

Language:

english

File:

PDF, 2.51 MB

english, 2014

14

Efficacy of a Combined Intracerebral and Systemic Gene Delivery Approach for the Treatment of a Severe Lysosomal Storage Disorder

Spampanato, Carmine, De Leonibus, Elvira, Dama, Paola, Gargiulo, Annagiusi, Fraldi, Alessandro, Sorrentino, Nicolina Cristina, Russo, Fabio, Nusco, Edoardo, Auricchio, Alberto, Surace, Enrico M, Balla

Journal:

Molecular Therapy

Year:

2011

Language:

english

File:

PDF, 671 KB

english, 2011

15

Systemic inflammation and neurodegeneration in a mouse model of multiple sulfatase deficiency

Settembre, C., Annunziata, I., Spampanato, C., Zarcone, D., Cobellis, G., Nusco, E., Zito, E., Tacchetti, C., Cosma, M. P., Ballabio, A.

Journal:

Proceedings of the National Academy of Sciences

Year:

2007

Language:

english

File:

PDF, 2.49 MB

english, 2007

16

The M-phase-promoting Factor Modulates the Sensitivity of the Ca2+ Stores to Inositol 1,4,5-Trisphosphate via the Actin Cytoskeleton

Lim, D., Ercolano, E., Kyozuka, K., Nusco, G. A., Moccia, F., Lange, K., Santella, L.

Journal:

Journal of Biological Chemistry

Year:

2003

Language:

english

File:

PDF, 1.24 MB

english, 2003

17

Impaired parkin-mediated mitochondrial targeting to autophagosomes differentially contributes to tissue pathology in lysosomal storage diseases

de Pablo-Latorre, R., Saide, A., Polishhuck, E. V., Nusco, E., Fraldi, A., Ballabio, A.

Journal:

Human Molecular Genetics

Year:

2012

Language:

english

File:

PDF, 569 KB

english, 2012

18

Correction of CNS defects in the MPSII mouse model via systemic enzyme replacement therapy

Polito, V. A., Abbondante, S., Polishchuk, R. S., Nusco, E., Salvia, R., Cosma, M. P.

Journal:

Human Molecular Genetics

Year:

2010

Language:

english

File:

PDF, 1005 KB

english, 2010

19

Phenylbutyrate Therapy for Pyruvate Dehydrogenase Complex Deficiency and Lactic Acidosis

Ferriero, R., Manco, G., Lamantea, E., Nusco, E., Ferrante, M. I., Sordino, P., Stacpoole, P. W., Lee, B., Zeviani, M., Brunetti-Pierri, N.

Journal:

Science Translational Medicine

Year:

2013

Language:

english

File:

PDF, 1.25 MB

english, 2013

20

FGF signalling regulates bone growth through autophagy

Cinque, Laura, Forrester, Alison, Bartolomeo, Rosa, Svelto, Maria, Venditti, Rossella, Montefusco, Sandro, Polishchuk, Elena, Nusco, Edoardo, Rossi, Antonio, Medina, Diego L., Polishchuk, Roman, De Ma

Journal:

Year:

2015

Language:

english

File:

PDF, 11.08 MB

english, 2015

21

Activated M-phase-promoting factor (MPF) is exported from the nucleus of starfish oocytes to increase the sensitivity of the Ins(1,4,5)P3 receptors

Santella, L., Ercolano, E., Lim, D., Nusco, G.A., Moccia, F.

Journal:

Biochemical Society Transactions

Year:

2003

Language:

english

File:

PDF, 120 KB

english, 2003

22

SUMF1 enhances sulfatase activities in vivo in five sulfatase deficiencies

Fraldi, Alessandro, Biffi, Alessandra, Lombardi, Alessia, Visigalli, Ilaria, Pepe, Stefano, Settembre, Carmine, Nusco, Edoardo, Auricchio, Alberto, Naldini, Luigi, Ballabio, Andrea, Cosma, Maria Pia

Journal:

Biochemical Journal

Year:

2007

Language:

english

File:

PDF, 483 KB

english, 2007

23

Low-dose gene therapy reduces the frequency of enzyme replacement therapy in a mouse model of lysosomal storage disease

Alliegro, Marialuisa, Ferla, Rita, Nusco, Edoardo, De Leonibus, Chiara, Settembre, Carmine, Auricchio, Alberto

Journal:

Molecular Therapy

Year:

2016

Language:

english

File:

PDF, 1.71 MB

english, 2016

24

280. Combination of Low-Dose Gene Therapy and Monthly Enzyme Replacement Therapy Improves the Phenotype of a Mouse Model of Lysosomal Storage Disease

Ferla, Rita, Alliegro, Marialuisa, Nusco, Edoardo, Claudiani, Pamela, Auricchio, Alberto

Journal:

Molecular Therapy

Year:

2015

Language:

english

File:

PDF, 273 KB

english, 2015

25

Non clinical safety and efficacy of a recombinant AAV2/8 vector administered intravenously for treatment of mucopolysaccharidosis type VI

Ferla, Rita, Alliegro, Marialuisa, Marteau, Jean-Brice, Dell'Anno, Margherita, Nusco, Edoardo, Pouillot, Severine, Galimberti, Stefania, Valsecchi, Maria Grazia, Zuliani, Vincent, Auricchio, Alberto

Journal:

Molecular Therapy — Methods & Clinical Development

Year:

2017

Language:

english

File:

PDF, 3.22 MB

english, 2017

26

AAV-mediated transcription factor EB (TFEB) gene delivery ameliorates muscle pathology and function in the murine model of Pompe Disease

Gatto, Francesca, Rossi, Barbara, Tarallo, Antonietta, Polishchuk, Elena, Polishchuk, Roman, Carrella, Alessandra, Nusco, Edoardo, Alvino, Filomena Grazia, Iacobellis, Francesca, De Leonibus, Elvira,

Journal:

Scientific Reports

Year:

2017

Language:

english

File:

PDF, 1.69 MB

english, 2017

27

Enhancement of hepatic autophagy increases ureagenesis and protects against hyperammonemia

Soria, Leandro R., Allegri, Gabriella, Melck, Dominique, Pastore, Nunzia, Annunziata, Patrizia, Paris, Debora, Polishchuk, Elena, Nusco, Edoardo, Thöny, Beat, Motta, Andrea, Häberle, Johannes, Ballabi

Journal:

Proceedings of the National Academy of Sciences

Year:

2017

Language:

english

File:

PDF, 1.46 MB

english, 2017

28

Pyruvate dehydrogenase complex and lactate dehydrogenase as targets for therapy of acute liver failure.

Ferriero, Rosa, Nusco, Edoardo, De Cegli, Rossella, Carissimo, Annamaria, Manco, Giuseppe, Brunetti-Pierri, Nicola

Journal:

Journal of Hepatology

Year:

2018

Language:

english

File:

PDF, 1.32 MB

english, 2018

29

Hepatic autophagy potentiates ureagenesis and its enhancement protects against acute and chronic hyperammonemia

Soria, L., Allegri, G., Melck, D., Pastore, N., Annunziata, P., Paris, D., Polishchuk, E., Nusco, E., Thöny, B., Motta, A., Häberle, J., Ballabio, A., Brunetti-Pierri, N.

Journal:

Journal of Hepatology

Year:

2018

Language:

english

File:

PDF, 82 KB

english, 2018

30

Inhibition of pyruvate dehydrogenase complex and lactate dehydrogenase for therapy of acute liver failure

Ferriero, R., Nusco, E., Cegli, R.D., Carissimo, A., Manco, G., Brunetti-Pierri, N.

Journal:

Journal of Hepatology

Year:

2018

Language:

english

File:

PDF, 196 KB

english, 2018

31

Disease Rescue and Increased Lifespan in a Model of Cardiomyopathy and Muscular Dystrophy by Combined AAV Treatments

Vitiello, Carmen, Faraso, Stefania, Sorrentino, Nicolina Cristina, Di Salvo, Giovanni, Nusco, Edoardo, Nigro, Gerardo, Cutillo, Luisa, Calabrò, Raffaele, Auricchio, Alberto, Nigro, Vincenzo, Lewin, Al

Journal:

Year:

2009

Language:

english

File:

PDF, 4.65 MB

english, 2009

32

Modelling TFE renal cell carcinoma in mice reveals a critical role of WNT signaling

Calcagnì, Alessia, kors, Lotte, Verschuren, Eric, De Cegli, Rossella, Zampelli, Nicolina, Nusco, Edoardo, Confalonieri, Stefano, Bertalot, Giovanni, Pece, Salvatore, Settembre, Carmine, Malouf, Gabrie

Journal:

Year:

2016

Language:

english

File:

PDF, 6.38 MB

english, 2016

33

microRNAs as biomarkers in Pompe disease

Tarallo, Antonietta, Carissimo, Annamaria, Gatto, Francesca, Nusco, Edoardo, Toscano, Antonio, Musumeci, Olimpia, Coletta, Marcella, Karali, Marianthi, Acampora, Emma, Damiano, Carla, Minopoli, Nadia,

Journal:

Genetics in Medicine

Year:

2018

Language:

english

File:

PDF, 1.76 MB

english, 2018

34

Enhancing the Therapeutic Potential of Sulfamidase for the Treatment of Mucopolysaccharidosis IIIA

Sorrentino, Nicolina Cristina, Cacace, Vincenzo, De Risi, Maria, Maffia, Veronica, Strollo, Sandra, Tedesco, Novella, Nusco, Edoardo, Romagnoli, Noemi, Ventrella, Domenico, Huang, Yan, Liu, Nan, Kalle

Journal:

Molecular Therapy — Methods & Clinical Development

Year:

2019

File:

PDF, 3.06 MB

2019

35

The amyloid self-assembly inhibitor CLR01 relieves autophagy and ameliorates neuropathology in a severe lysosomal storage disease

Monaco, Antonio, Maffia, Veronica, Sorrentino, Nicolina Cristina, Sambri, Irene, Ezhova, Yulia, Giuliano, Teresa, Cacace, Vincenzo, Nusco, Edoardo, De Risi, Maria, De Leonibus, Elvira, Schrader, Thoma

Journal:

Molecular Therapy

Year:

2020

File:

PDF, 44.60 MB

2020

36

Retinal Degeneration in MPS-IIIA Mouse Model

Intartaglia, Daniela, Giamundo, Giuliana, Marrocco, Elena, Maffia, Veronica, Salierno, Francesco Giuseppe, Nusco, Edoardo, Fraldi, Alessandro, Conte, Ivan, Sorrentino, Nicolina Cristina

Journal:

Frontiers in Cell and Developmental Biology

Year:

2020

Language:

english

File:

PDF, 6.78 MB

english, 2020

37

Lightâresponsive microRNA miRâ211 targets Ezrin to modulate lysosomal biogenesis and retinal cell clearance

Naso, Federica, Intartaglia, Daniela, Falanga, Danila, Soldati, Chiara, Polishchuk, Elena, Giamundo, Giuliana, Tiberi, Paola, Marrocco, Elena, Scudieri, Paolo, Di Malta, Chiara, Trapani, Ivana, Nusco,

Journal:

The EMBO Journal

Year:

2020

File:

PDF, 9.64 MB

2020

38

CHOP and c-JUN upregulate the mutant Z alpha-1 antitrypsin, exacerbating its aggregation and liver proteotoxicity.

Attanasiio, Sergio, Ferriero, Rosa, Gernoux, Gwladys, De Cegli, Rossella, Carissimo, Annamaria, Nusco, Edoardo, Campione, Severo, Teckman, Jeffrey, Mueller, Christian, Piccolo, Pasquale, Brunetti-Pier

Journal:

Journal of Biological Chemistry

Year:

2020

File:

PDF, 1.46 MB

2020

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